Acute Regulatory Protein (StAR)

Female external genitalia in males and females
Failure to grow
Florid lipid deposits in adrenal cortex
Death from adrenocortical insufficiency

Reference:

Caron KM, Soo SC, Wetsel WC, Stocco DM, Clark BJ, Parker KL.: Targeted disruption of the mouse gene encoding steroidogenic acute regulatory protein provides insights into congenital lipoid adrenal hyperplasia. Pro Natl Acd Sci USA 1997 Oct 14;94 (21):111540-11545.